ANAG rabbit pAb
ENT-A14280
Description
| REF | ENT-A14280 |
|---|---|
| Category | Antibody Polyclonal |
| Description | ANAG rabbit pAb |
| Source | Rabbit |
| Applications | WB |
| Reactivity | Human;Rat;Mouse; |
| Reactivity | Human;Rat;Mouse; |
| Dilution | WB 1：500-2000 |
| Immunogen | Synthesized peptide derived from human ANAG AA range: 146-196 |
| Storage Stability | -20°C/1 year |
| Clonality | Polyclonal |
| Isotype | IgG |
| Concentration | 1 mg/ml |
| Observed Band KD | |
| Human Gene ID | 4669 |
| Human Swiss Prot Nº | P54802 |
| Subcellular Location | Lysosome. |
Other Name:
Background: This gene encodes an enzyme that degrades heparan sulfate by hydrolysis of terminal N-acetyl-D-glucosamine residues in N-acetyl-alpha-D-glucosaminides. Defects in this gene are the cause of mucopolysaccharidosis type IIIB (MPS-IIIB), also known as Sanfilippo syndrome B. This disease is characterized by the lysosomal accumulation and urinary excretion of heparan sulfate. [provided by RefSeq, Jul 2008],